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Apostolos G. Pitoulias (Department of Vascular and Endovascular Surgery Research Vascular Center Asklepios Clinic Langen Langen Germany) Nizar Abu Bakr (Department of Vascular and Endovascular Surgery Research Vascular Center Asklepios Clinic Langen Langen Germany) Majid Kazemtash (Department of Vascular and Endovascular Surgery Research Vascular Center Asklepios Clinic Langen Langen Germany) Firouza Dahi (Department of Vascular and Endovascular Surgery Research Vascular Center Asklepios Clinic Langen Langen Germany) Michael Schütz (Department of Vascular and Endovascular Surgery Research Vascular Center Asklepios Clinic Langen Langen Germany) Konstantinos P. Donas (Department of Vascular and Endovascular Surgery Research Vascular Center Asklepios Clinic Langen Langen GermanyDepartment of Vascular Surgery Bern University Hospital Bern Switzerland)
저널정보
대한혈관외과학회 Vascular Specialist International Vascular Specialist International Vol.39 No.2
발행연도
2023.6
수록면
14 - 14 (1page)
DOI
10.5758/vsi.230017

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Von Gierke disease, also known as glycogen storage disease type I, co-existent with an abdominal aortic aneurysm (AAA), is an extremely rare combination of diseases that requires challenging therapeutic measures. We present, for the first time in literature, the case of a 62-year-old female with von Gierke disease who required open surgical repair of an AAA with challenging neck anatomy outside of instructions for use of endovascular repair. Even though the surgical risks for lifethreatening complications, such as pancreatitis, metabolic acidosis, and kidney failure, were high, the 6-month postoperative course was uneventful. Despite the invasiveness of the treatment, surgery to treat the AAA was safe and effective. Further data is needed to draw robust conclusions about the treatment of choice for those patients with diseases in co-existence with AAAs.

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